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Open Access Case Report

Tufted angioma (Angioblastoma) of eyelid in adults-report of two cases

Ruchi Mittal1* and Devjyoti Tripathy2

Author Affiliations

1 Dalmia Ophthalmic Pathology Services, L.V. Prasad Eye Institute, Bhubaneswar, Orissa, India

2 Department of Ophthalmic Plastic Surgery, Orbit and Ocular Oncology, L.V. Prasad Eye Institute, Bhubaneswar, Orissa, India

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Diagnostic Pathology 2013, 8:153  doi:10.1186/1746-1596-8-153

Published: 17 September 2013

Abstract

Tufted angioma, first recognized in Japanese literature as “Angioblastoma of Nagakawa”, is a rare benign vascular tumour with a variable clinical presentation. It commonly manifests as a macule, papule or nodule in infancy or childhood in the region of the upper trunk and neck. Here in we report two cases of this rare progressive angioma as lesions of the eyelid in adults. Tufted angioma has a classical “cannon ball” like appearance of vascular tufts on histopathology. Immunohistochemical staining with actin highlights the spindly stromal cells surrounding the capillaries. Complete physical examination and haematological work up is recommended in patients with tufted angioma to exclude rare association of port wine stain and Kasabach-Merritt syndrome with this rare entity. To the best of our knowledge, our cases illustrate the first case report of tufted angioma presenting as an eyelid lesion.

The virtual slide(s) for this article can be found here: http://www.diagnosticpathology.diagnomx.eu/vs/1230909536950947 webcite.

Keywords:
Tufted angioma; Angioblastoma; Eyelid; Adults; Kasabach-Merritt syndrome