Table 1

Vulvar proximal type epithelioid sarcoma: the current literature review
Author Year Age Surgery RT CT Recurrent site DFS (months) OS (months)
Piver SM et al. [4] 1972 1 27 Wide local excision No No None - NED (108)
Gallup DG et al. [6] 1976 1 31 Radical vulvectomy No No None - NED (16)
Hall DJ et al. [7] 1980 1 31 Wide local excision, inguinal lymph node dissection No No Local, lymph node, lung 35 DOD (70)
Ulbright TM et al. [8] 1983 2 55 Local excision No No Local, lung, abdominal wall, skin 8 DOD (15)
30 Wide local excision No Yes Local, Lung 2 DOD (8)
Tan GWT et al. [9] 1989 1 21 Wide local excision No No None - NED (36)
Perrone T et al. [10] 1989 1 21 Local excision, lymph node dissection No No None - NED (56)
Wevers AC et al. [11] 1989 1 21 Local excision, lymph node dissection No No Local recurrence 2 DOD (5)
Weissmann D et al. [12] 1990 1 26 Local excision No No Local lymph node, lung, scalp, liver, kidney 14 AWD (78)
Hernandez-Ortiz MJ et al. [13] 1995 1 51 Radical vulvectomy No No Lung 5 DOD (8)
Konefka T et al. [14] 1994 1 49 Radical vulvectomy and bilateral inguinal lymph node dissection No Yes Lung 5 DOD (8)
Guillou L et al. [15] 1997 3 57 Local excision Yes No None - DOID (52)
49 Radical vulvectomy Yes No None - NED (22)
45 Wide local excision No Yes None - NED (21)
Tjalma WA et al. [16] 1999 1 23 Hemivulvectomy No No None - NED (48)
Kasamatsu T et al. [17] 2001 1 23 Local excision No No Local lymph node 96 NED
2001 3 37 Local excision No Yes None - NED (11)
30 Local excision No No Local lymph node, skin 96 NED (104)
80 Wide local excision No No Local lymph node, lung 16 DOD (23)
Altundag K et al. [5] 2004 1 51 Left hemivulvectomy with bilateral inguinal lymph node dissection No Yes Lung 4 DOD (6)
Dainese E et al. [19] 2005 1 34 Right emivulvectomy with right inguinal lymph node dissection No No None - NED (12)
Argenta PA et al. [20] 2007 1 35 Radical excision, inguinal-femoral lymph node dissection Yes No None - NED (40)
Kim JH et al. [21] 2008 1 24 Clitoris sparing wide local excision No No None - NED (8)
Rai H et al. [22] 2009 1 17 Local excision, lymph node dissection Yes No Local lymphnode 2 AWD (2)
Tholpady A et al. [23] 2010 1 17 Radical excision No No - - NED (12)
Chiyoda T et al. [24] 2011 1 33 Left radical vulvectomy No No None - NED (36)
Andrisani A et al. [25] 2011 1 46 Radical superior vulvectomy Yes Yes Local lymph nodes, abdominal wall, genital, inguinal and thigh muscles, bladder 1 DOD (11)
Kim HJ et al. [26] 2012 1 41 Local excision No No None - NED (10)
Ong AC et al. [27] 2012 1 51 Right emivulvectomy and right inguinal lymph node dissection No No None - NED (8)
Our study 1 63 Bilateral radical vulvectomy, right inguinal lymph node dissection Yes No Inguinal lymph node - NED (14)

NED no evidence of disease, DOD dead of disease, DOID dead of inter current disease, AWD alive with disease, RT radiotherapy, CT chemotherapy, DFS disease free survival, OS overall survival.

Patrizi et al.

Patrizi et al. Diagnostic Pathology 2013 8:122   doi:10.1186/1746-1596-8-122

Open Data