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Open Access Case Report

Postauricular congenital alveolar rhabdomyosarcoma- a case report of an unusual entity

Mahesha Vankalakunti1, Ashim Das1* and Narasimhan KL Rao2

Author Affiliations

1 Department of Histopathology, Postgraduate Institute of Medical Education & Research, Chandigarh, India

2 Department of Pediatric surgery, Postgraduate Institute of Medical Education & Research, Chandigarh, India

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Diagnostic Pathology 2006, 1:37  doi:10.1186/1746-1596-1-37

Published: 17 October 2006

Abstract

Background

Congenital alveolar rhabdomyosarcoma is an extremely uncommon and invariably fatal tumor with the current therapy. Less than 25% of patients present with evidence of cutaneous metastasis.

Case presentation

We report a case of congenital alveolar rhabdomyosarcoma in an 18-month-old male who presented with a progressively increasing mass lesion in the left post-auricular region since birth. Radiological examination did not show any intracranial involvement of the mass lesion. Upon resecting the mass that was 10-cm in largest dimension, the gross, microscopic, and ultrastructural findings were consistent with congenital alveolar rhabdomyosarcoma.

Conclusion

The suspicion of alveolar subtype on histological grounds and proper evaluation of this tumor by immunostain and ultrastuctural examination is necessary. In the Medline literature search, there is no report of large congenital alveolar rhabdomyosarcoma in the post-auricle region.